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The clinical manifestations included intensive breathlessness and dyspnea (n=30,88.2%) and amyctic cough (n=29, 85.3%), hemoptysis (n=14, 41.2%). 病變部位累及氣琯18例,累及右主支氣琯15例,累及左主支氣琯9例,累及段及以下支氣琯5例。